Late-onset erythromelalgia in a previously healthy young woman: a case report and review of the literature
نویسندگان
چکیده
INTRODUCTION Erythromelalgia is a rare disorder characterized by episodic erythema and burning pain, which commonly involves the extremities. We present a case of late onset erythromelalgia in a previously healthy young woman and briefly review the literature. Our patient's case also has additional uncommon features not reported previously. CASE PRESENTATION A 33-year-old previously healthy Caucasian woman presented with complaints of episodic burning pain and flushing occurring in a central distribution involving her face, ears, upper chest and, occasionally, her upper extremities. Her symptoms were triggered by lying down or warm temperature exposure and were relieved by cooling measures. Extensive diagnostic work-up looking for secondary causes for the symptoms was negative and the diagnosis of erythromelalgia was made based on details provided in her clinical history supported by raised temperature in the affected area measured by thermography during a symptomatic episode. The patient did not respond to pharmacological therapy or surgical sympathectomy. She was advised on lifestyle modification to avoid activities which triggered her symptoms. She was hypothermic with a core temperature between 92 and 95 degrees F. She also had premature ovarian failure, which had not previously been reported. CONCLUSION Erythromelalgia is a rare disorder of unknown cause. There is no confirmatory diagnostic test; diagnosis is based on details provided in the patient's medical history and physical examination during the episodes. For those affected, this disorder leads to significant long-term morbidity and unfortunately, to date, no definitive therapy is available except for lifestyle modification.
منابع مشابه
A 30-year-old healthy man with recent onset erythromelalgia: A case report
A 30-year-old healthy man came to our hospital with complaints of red, hot, and painful upper extremities which spontaneously appeared. These manifestations worsened with exercises and heat, but were alleviated by rest and cooling of the hands. There were 2 similar previous episodes of short duration. The patient was a healthy, non-alcoholic, non-smoker with no history of using medicine. ...
متن کاملProlonged Hemoptysis Caused by Primary Pulmonary Epithelioid Hemangioendothelioma; A Case Report and Review of the Literature
Epithelioid hemangioendothelioma is a vascular tumor with an intermediate malignant potential. This tumor is very rare in the lung parenchyma, and most of the previously reported cases have been asymptomatic. There is no standard therapy for this tumor and prognosis in the previous reports has been variable.Herein we report our experience with a 60-year-old woman presenting with hemoptysis and ...
متن کاملBilateral C5 Palsy Following a Circumferential Surgery for Cervical Spondylotic Myelopathy: Case Report and Review (In press)
Background and Importance: The development of C5 root palsy is a well-known potential complication of cervical spine surgeries for the correction of cervical spondylotic myelopathy. It typically occurs unilaterally but on extremely rare occasions it might occur as a bilateral anomaly. The value of intraoperative neurophysiologic monitoring in detection of iatrogenic acute versus delayed onset C...
متن کاملZYGOMYCOSIS OF COLON CASE REPORT AND REVIEW OF THE LITERATURE
Zygomycosis is a fulminant infection which usually afflicts patients who are immunocompromised by diabetes mellitus, malignancy or immunosuppressive therapy.l This disease is a rare but highly invasive fungal infection which occurs in organ transplant recipients. 2 Mucormycosis confined to the gastrointestinal tract is an uncommon form of the disease. accounting for only seven percent of al...
متن کاملProsthetic valve endocarditis caused by multidrug-resistant Candida albicans in a patient with myelodysplasia syndrome: A case report and literature review
Background and Purpose: Candida endocarditis is an infrequent disease with a high mortality rate, which commonly occurs in immunosuppressed patients with cardiac valve replacement. We reported a 70-year-old woman diagnosed with Candida prosthetic valve endocarditis (PVE). This study also involved a review of all published cases of Candida PVE from 1970. Case report: Herein, we reported a 70-ye...
متن کامل